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Factor V deficiency

Synonym(s)

  • accelerator globulin deficiency
  • AC globulin deficiency
  • deficiency, labile
  • hereditary factor V deficiency disease
  • hereditary hypoproaccelerinemia
  • labile factor deficiency
  • Owren disease
  • parahemophilia
  • proaccelerin deficiency

Definition(s)

A deficiency of blood coagulation factor V (known as proaccelerin or accelerator globulin or labile factor) leading to a rare hemorrhagic tendency known as Owren's disease or parahemophilia. It varies greatly in severity. Factor V deficiency is an autosomal recessive trait. (Dorland, 27th ed)

Definition from: Unified Medical Language SystemThis link leads to a site outside Genetics Home Reference. (MeSH)   at the National Library of Medicine

 
Published: January 23, 2009