| Topic: | hematologic diseases (he) |
| Title: | Factor XI Deficiency: An Inherited Bleeding Disorder. |
| Author: | Amesse, C., et al. |
| Source: | Montreal, QC: Canadian Hemophilia Society. 2007. 24 p. |
| Availability: | Available from Canadian Hemophilia Society. 625 President Kennedy, Suite 505, Montreal, QC, H3A 1K2. Phone: 1-800-668-2686. Email: chs@hemophilia.ca. Website: www .hemophilia.ca. |
| Abstract: | This document provides comprehensive information about Factor XI deficiency, a rare blood coagulation disorder. The authors review the history of this disorder, which was described in 1953, and consider the transmission of Factor XI deficiency, which is an inherited disorder. A series of charts show the percentage possibility of passing on the disorder, depending on the genes carried by each parent. Additional topics describe normal blood clotting and the role of coagulation factors, the incidence of Factor XI deficiency, diagnostic strategies, symptoms, problems specific to women with Factor XI deficiency, and treatment options. A variety of treatment and prevention options are available, including fresh frozen plasma, Factor XI concentrate, hormone therapy, desmopressin (DDAVP), and tranexamic acid––Cyklokapron. One section offers practical strategies for preventing excessive bleeding during dental care and reviews first aid to be administered in common situations such as nosebleeds. People with Factor XI are advised to wear a medical identification tag, to be vaccinated regularly, and to work closely with their team of health care providers. The document concludes with the contact information for the Canadian Hemophilia Society and a bibliography. 6 figures. 12 references. |
| Format: | Monograph/Book |
| Language: | English. |
| Major Keywords: | Hematologic Diseases. Hemophilia C. Bleeding Disorders. Symptoms. Diagnosis. Patient Care Management. Therapy. |
| Minor Keywords: | Patient Education. Diagnostic Tests. Heredity. Genetics. Hemorrhage. Menstruation. Dental Care. Patient Care Team. Emergencies. First Aid. |
| Publication Number: | HEBK10189. |
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