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Childhood disintegrative disorder

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Contents of this page:

Illustrations

Motormental retardation
Motormental retardation

Alternative Names    Return to top

Disintegrative psychosis; Heller syndrome

Definition    Return to top

Childhood disintegrative disorder is a condition occurring in 3- and 4-year-olds who have developed normally to age 2. Over several months, a child with this disorder will deteriorate in intellectual, social, and language functioning from previously normal behavior.

Causes    Return to top

The cause of childhood disintegrative disorder is unknown, but it has been linked to neurological problems. An affected child shows a loss of communication skills, has regression in nonverbal behaviors, and significant loss of previously-acquired skills. The condition is very similar to autistic disorder (autism).

Symptoms    Return to top

Exams and Tests    Return to top

This disorder must be differentiated from both childhood schizophrenia and pervasive developmental disorder (autism).

The most important signs of childhood disintegrative disorder are loss of developmental milestones. The child tends to have normal development through age 3 to 4 and then over a few months undergoes a gradual loss of previously established abilities (e.g., language, motor, or social skills). Generally, the diagnosis is made with a loss of functioning in at least two areas described above.

Treatment    Return to top

Treatment is the same for autistic disorder (autism) because of the similarity in the two disorders.

Outlook (Prognosis)    Return to top

Unfortunately, the prognosis for this disorder is limited. The loss of functioning will likely be permanent. However, to some degree, behaviors can be modified.

When to Contact a Medical Professional    Return to top

Call your provider if your child has any delays in development or starts to lose developmental abilities.

Update Date: 6/13/2006

Updated by: Benjamin W. Van Voorhees, MD, MPH, Assistant Professor of Medicine and Pediatrics, The University of Chicago, Chicago, IL. Review provided by VeriMed Healthcare Network.

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