Genetic and Rare Diseases Information Center (GARD)


Other names people use for this condition
  • MPS type 1
  • Attenuated MPS I (subtype)
  • Severe MPS I (subtype)
  • Hurler syndrome (former subtype)
  • Hurler-Scheie syndrome (former subtype)
  • Scheie syndrome (former subtype; formerly known as Mucopolysaccharidosis type V)
  • Alpha-L-Iduronidase deficiency
  • IDUA deficiency

Mucopolysaccharidosis I
Please note that the links contained on this search results page may take you to sites outside of the NIH. (See Disclaimer under Site Policies for details.)


Mucopolysaccharidosis I (MPS I) is a condition that affects many different parts of the body. It is a progressively debilitating disorder; however, the rate of progression varies among affected individuals. MPS I is caused by reduced levels or the complete lack of the IDUA enzyme. Without the proper amount of this enzyme, many different organs and tissues of the body become enlarged, resulting in various medical problems. This condition is usually divided into two subtypes, severe MPS I and attenuated MPS I. While both types can cause similar symptoms, people with severe MPS I typically have an earlier onset of symptoms, a decline in intellectual function, and a shorter lifespan. Although there is no cure for MPS I, bone marrow transplant and enzyme replacement therapy are treatment options that may help manage the symptoms of this condition.[1]

References
  1. Clarke LA. Mucopolysaccharidosis Type I. Gene Reviews. September 21, 2007 Available at: http://www.ncbi.nlm.nih.gov/bookshelf/br.fcgi?book=gene&part=mps1. Accessed July 15, 2008.

For more information about Mucopolysaccharidosis I click on the boxes below:
Q&A More
Information
Support
Groups
Research &
Clinical Trials
Services More Search
Tools

Questions & Answers (Found: 1 Resources)
A list of questions from the public on rare and/or genetic diseases that have been answered by the Genetic and Rare Disease Information Center. Click on each question to find the answer.

   Click arrows to expand or collapse a Resource Section.
   Show All Resources   Hide All Resources




Note: If you need help accessing information in different file formats such as PDF, MP3, see Viewers, Players, and Plug-ins.