Genetic and Rare Diseases Information Center (GARD)


Other names people use for this condition
  • Desmoplastic supratentorial neuroepithelial tumors of infancy

Desmoplastic infantile ganglioma
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Desmoplastic infantile gangliomas (DIGs) are rare brain tumors that are normally located in the frontal or parietal lobes of the brain.  They are are usually diagnosed before 18 months of age with most infants presenting with a short duration of symptoms.  Although seizures are not commonly observed, a bulging fontanelle, rapid head growth, vomiting, and a sunset sign are usually noted.  The standard treatment for DIGs is surgical resection (surgical procedure in which the portion of the brain with the tumor is removed).  [1]

References
  1. Smith SH. Textbook of Uncommon Cancer. 3rd ed. In: . Uncommon Pediatric Brain Tumors. England:John Wiley & Sons Ltd; 2006:

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